A Rare Case of Sphenoid Sinus Mesenchymal Chondrosarcoma: A Diagnostic Challenge
International Journal of Otorhinolaryngology
Volume 1, Issue 1, September 2015, Pages: 9-12
Received: Sep. 1, 2015; Accepted: Sep. 14, 2015; Published: Sep. 14, 2015
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Authors
Ahmad Kusyairi Bin Khalid, Department of Otorhinolaryngology-Head and Neck Surgery, Universiti Teknologi MARA (UiTM), Sungai Buloh Campus, Jalan Hospital, Selangor, Malaysia
Haizlene Abd Halim, Department of Primary Care Medicine, Universiti Teknologi MARA (UiTM), Sungai Buloh Campus, Jalan Hospital, Selangor, Malaysia
Balwant Singh Gendeh, Department of Otorhinolaryngology-Head and Neck Surgery, Universiti Kebangsaan Malaysia (UKM), Jalan Yaacob Latif, Bandar Tun Razak, Cheras, Wilayah Persekutuan Kuala Lumpur, Malaysia
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Abstract
Mesenchymal chondrosarcoma (MC) is a subtype of chondrosarcoma which is rarely encountered in the clinical practice. It carries a worse prognosis compared to other forms of chondrosarcoma as it has a high tendency to metastasize to other sites.1 It can arise from skeletal bone as well as soft tissue, the usual sites being the ribs and jaw.2 Histologically, it is characterized by a mix of cartilage and undifferentiated stromal tissue, which will be highly positive for S100. A survey done concluded that it commonly affects patients in their second or third decade of life.3 We will discuss a rare case of MC which presented to our center where the initial biopsy was reported as hemangiopericytoma (HPC) of nose. The tumour was excised using endoscopic assisted craniofacial resection (EACFR). A multidisciplinary team comprising of various specialties was involved in diagnosing and managing the patient.
Keywords
Mesenchymal Chondrosarcoma, Sphenoid Sinus Tumour
To cite this article
Ahmad Kusyairi Bin Khalid, Haizlene Abd Halim, Balwant Singh Gendeh, A Rare Case of Sphenoid Sinus Mesenchymal Chondrosarcoma: A Diagnostic Challenge, International Journal of Otorhinolaryngology. Vol. 1, No. 1, 2015, pp. 9-12. doi: 10.11648/j.ijo.20150101.13
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