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First European Case of TAFRO Syndrome Associated with Sjogren Disease
American Journal of Internal Medicine
Volume 2, Issue 6, November 2014, Pages: 102-105
Received: Jul. 3, 2014; Accepted: Nov. 5, 2014; Published: Nov. 20, 2014
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Lynn Antoun Abdo, Internal medicine department, Saint Antoine Hospital, Paris, France
Clement Philippe Morin, Internal medicine department, Saint Camille Hospital, Bry-sur-Marne, France
Rocco Paolo Collarino, Infectious disease department, Tenon hospital, Paris, France
Jean Paul Cabane, Internal medicine department, Saint Antoine Hospital, Paris, France
Marc Albert Gatfosse, Internal medicine department, Saint Antoine Hospital, Paris, France
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We herein describe a case of an unusual multicentric castleman disease(MCD) accompanied by Thrombocytopenia, Anasarca, myeloFibrosis and Renal failure, compatible with TAFRO syndrome and associated with Sjogren disease. The treatment with corticosteroids dramatically improved the symptoms. The clinical features of this case were similar to those reported previously in Japan but this appears to be the first European MCD with negative HHV8 and HIV that meets the criteria of TAFRO syndrome, associated with Sjögren disease.
TAFRO Syndrome, Sjogren Disease, Castleman Disease, Interleukin-6, Thrombocytopenia, Pleural Effusion
To cite this article
Lynn Antoun Abdo, Clement Philippe Morin, Rocco Paolo Collarino, Jean Paul Cabane, Marc Albert Gatfosse, First European Case of TAFRO Syndrome Associated with Sjogren Disease, American Journal of Internal Medicine. Vol. 2, No. 6, 2014, pp. 102-105. doi: 10.11648/j.ajim.20140206.12
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