Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis
American Journal of Internal Medicine
Volume 6, Issue 5, September 2018, Pages: 94-98
Received: Jun. 27, 2018;
Accepted: Jul. 23, 2018;
Published: Aug. 24, 2018
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Arti Sharma, Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India
Abhay Uppe, Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India
Shahid Patel, Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India
Girija Nair, Department of Pulmonary Medicine, D. Y. Patil Medical College, Navi Mumbai, India
Pulmonary alveolar microlithiasis (PAM) is a rare autosomal recessive disease, characterised by widespread intra-alveolar accumulation of microliths. A 30-year-old male patient, known case of rheumatioid arthritis on treatment, presented with occasional complaints of cough with expectoration, since 1 year. He was found to be sputum AFB positive for which AKT was started, and a chest xray was advised, which showed diffuse bilateral micronodular calcific opacities having sand-like appearance distributed throughout the lungs, with a evident black pleural sign, which made us suspect PAM. An HRCT chest showed, multiple dense micronodular opacities in bilateral lung parenchyma prominently in the middle and lower lung zones giving a classical sandstorm appearance with sparing of a thin peripheral subpleural rim of parenchyma, giving a black pleura sign. The patient was symptomatically treated and was counselled for lung transplant and presents for regular follow up.
Pulmonary Alveolar Microlithiasis and Rheumatoid Arthritis with Pulmonary Tuberculosis, American Journal of Internal Medicine.
Vol. 6, No. 5,
2018, pp. 94-98.
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